Pathways of ammonia detoxification to GLN in muscles affiliated with Increased use from the BCAA and ?-KG (cataplerosis) and proposed outcomes of BCAA and phenylbutyrate in subjects with liver cirrhosis or UCD. Beneficial outcome of BCAA on ammonia detoxification to GLN may be blunted by GLN degradation to ammonia in enterocytes and kidneys. Phenyl